 |
 |
 |
Hemophilia Disease And Cells
Hemophilia is a genetic disorder which damages the body’s ability to control coagulation. Certain genetic deficiencies and rare autoimmune disorders may lower plasma clotting factor levels of the coagulation factors in the blood which are required for normal clotting process, and this leads to hemophilia.
In normal people when a blood vessel ruptures, a temporary scab forms. However, in hemophilia the coagulation factors are missing and this prevents the formation of fibrin which required for clotting and hence the temporary scab does not form. It is not hemophiliacs bleed more than normal people. The difference is that they bleed for a longer duration. Severe hemophilia can lead to bleeding for days, or weeks even from a small injury. The health risk in hemophilia comes from small cuts and injuries taking a long time to heal, and this can be fatal if the injury occurs in the brain or joints. Hemophilia increases the chances of re-bleeding and internal bleeding into muscles, joints and closed spaces after an external injury.
Since this is a genetic disorder, there is no cure for hemophilia but the disease can be controlled with regular infusions of the deficient clotting factor. Sometime, people suffering from hemophilia develop antibodies to the replaced clotting factor. They require increased amount of infusions and replacement with non-human products.
Usually people with hemophilia receive two types of care for their condition. One is prophylaxis and the other is on-demand. Prophylaxis is the infusion of clotting factor at regular intervals so that clotting levels in the blood are always maintained at high levels. On-demand refers to the treat that is given to people with hemophilia when a bleeding episode occurs.
Related Topics:
- Case Management of Hemophilia
- Health Coverage And Hemophilia Insurance
